CTNS monoclonal antibody (M09), clone 5G6
产品名称： CTNS monoclonal antibody (M09), clone 5G6
英文名称： CTNS monoclonal antibody (M09), clone 5G6
产品编号： H00001497-M09
产品价格： null
产品产地： 台湾
品牌商标： Abnova
更新时间： null
使用范围：
亚诺法生技股份有限公司（Abnova)
- 联系人 :
- 地址 : 台湾台北市内湖区洲子街 108 号 9 楼
- 邮编 : 11493
- 所在区域 : 台湾
- 电话 : +886-920**1152 点击查看
- 传真 : 点击查看
- 邮箱 : sales@abnova.com.tw
- Specification
- Product Description:
- Mouse monoclonal antibody raised against a partial recombinant CTNS.
- Immunogen:
- CTNS (NP_004928, 1 a.a. ~ 100 a.a) partial recombinant protein with GST tag. MW of the GST tag alone is 26 KDa.
- Sequence:
- MIRNWLTIFILFPLKLVEKCESSVSLTVPPVVKLENGSSTNVSLTLRPPLNATLVITFEITFRSKNITILELPDEVVVPPGVTNSSFQVTSQNVGQLTVY
- Host:
- Mouse
- Reactivity:
- Human, Mouse, Rat
- Isotype:
- IgG2a Kappa
- Storage Buffer:
- In 1x PBS, pH 7.2
- Storage Instruction:
- Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
- Quality Control Testing:
- Antibody Reactive Against Recombinant Protein.
Western Blot detection against Immunogen (36.74 KDa) .
- MSDS:
Download
- Publication Reference
- 1.
- Modulation of CTNS Gene Expression By Intracellular Thiols.
Bellomo F, Corallini S, Pastore A, Palma A, Laurenzi C, Emma F, Taranta A.Free Radic Biol Med. 2010 Jan 14. [Epub ahead of print]
- Applications
- Western Blot (Tissue lysate)
- CTNS monoclonal antibody (M09), clone 5G6. Western Blot analysis of CTNS expression in human liver.
- Protocol Download
- Western Blot (Cell lysate)
- CTNS monoclonal antibody (M09), clone 5G6. Western Blot analysis of CTNS expression in PC-12.
- Protocol Download
- Western Blot (Cell lysate)
- CTNS monoclonal antibody (M09), clone 5G6. Western Blot analysis of CTNS expression in HepG2.
- Protocol Download
- Western Blot (Cell lysate)
- CTNS monoclonal antibody (M09), clone 5G6. Western Blot analysis of CTNS expression in Raw 264.7.
- Protocol Download
- Western Blot (Recombinant protein)
- Protocol Download
- Sandwich ELISA (Recombinant protein)
- Detection limit for recombinant GST tagged CTNS is approximately 0.3ng/ml as a capture antibody.
- Protocol Download
- Entrez GeneID:
- 1497
- GeneBank Accession#:
- NM_004937
- Protein Accession#:
- NP_004928
- Gene Name:
- CTNS
- Gene Alias:
- CTNS-LSB,PQLC4
- Gene Description:
- cystinosis, nephropathic
- Gene Ontology:
- Hyperlink
- Gene Summary:
- This gene encodes a seven-transmembrane domain protein that functions to transport cystine out of lysosomes. Its activity is driven by the H+ electrochemical gradient of the lysosomal membrane. Mutations in this gene cause cystinosis, a lysosomal storage disorder. Alternative splicing results in multiple transcript variants. [provided by RefSeq
- Other Designations:
- -
- Gene Pathway
- Related Disease