重组人β-Galactosidase(β半乳糖苷酶)

中文名称：重组人β-Galactosidase(β半乳糖苷酶)
英文名称：Recombinant Human beta-Galactosidase
产品规格：10μg|50μg|500μg|1mg
本品由我们的哺乳动物细胞表达系统制备而成，目的基因编码的Leu24-Val677在C端含有His标签。

β-Galactosidase质量控制：＞95%(还原性SDS-PAGE)

β-Galactosidase制剂：液体

β-Galactosidase保存：收到货后请置于-20℃，可保存6个月，避免反复冻融。

关于β-Galactosidase：
β Galactosidase is a lysosomal β Galactosidase that hydrolyzes the terminal β Galactose from Ganglioside and Keratan sulfate. In lysosome, the mature β Galactosidase protein associates with Cathepsin A and Neuraminidase 1 to form the lysosomal multienzyme complex . An alternative splicing at the RNA level of β Galactosidase results a catalytically inactive β Galactosidase that plays an important role in vascular development. Defects of β-galactosidase (GLB1) are the cause of diseases like GM1-gangliosidosis which is a lysosomal storage disease and Morquio Syndrome B that cause patients to have abnormal elastic fibers. More than 100 mutations have been identified for β Galactosidase, which result in different residual activities of the mutant enzymes and a spectrum of symptoms in the two related diseases. 

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